PP135 : A rare case of cleft number nine associated with atypical cleft number two.

Dr.Linda Maria gdp

Introduction:Incidence of craniofacial cleft is rare ranging between 1.43 and 4.85 per 100,000 births. Tessier number nine cleft being the rarest, there are few reports of detailed ophthalmologic examinations performed in them.Case report: In our study a one-day-old female neonate delivered by normal vaginal delivery at term, weighing 1,480 gm presented with right eye dystopia, cleft extending through the lateral third of the upper eyelid, brow ending at the temporal region, conjunctival congestion, clear cornea 10mm in diameter, normal anterior chamber, pupil 2mm reactive to light, clear lens and normal fundus. Cleft extended downwards from the right medial canthus involving the nasal ala and left forearm had an oblique-crease with camptodactyly.Amniotic band syndrome being a possible cause.Conclusion:Our study describes the ophthalmic management of Tessier number nine cleft and thus, may be helpful in counselling and estimating the impact of this syndrome on the eye when in utero.