Dr.Prabhakara Sastry Papaganti
PURPOSE: To report about 8 cases of non progressive bilateral hereditary macular corneal dystrophy in a family which is unusual.
METHODS : We have studied 8 cases of non progressive bilateral hereditary macular corneal dystrophy in a family. No extraocular abnormalities have been associated with this disorder in all of them. Mother is having corneal distrophy and her all children except one male got effected with corneal distrophy. Out of 8 children 6 are males 2 are females. 2 females and 5 males are effected. Sympotms are like ocational FB sensation, photophobia, glare, and redness due to secondary infections. All these cases did not show any progress in the corneal leasions which is unusal. Family tree has been drawn and the disease is coming from mother side. 1st & 2nd degree siblings are also effected.
CONCLUSION : Non progressive bilateral hereditary macular corneal dystrophy in a joint family effecting nearly 21 members has been reported here which is unusual.
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